ICD-10-CM Codes 2026 (USA)

• E79.81	Aicardi-Goutieres syndrome

• E79.0	Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
  E79.1	Lesch-Nyhan syndrome
  E79.2	Myoadenylate deaminase deficiency
  E79.8	Other disorders of purine and pyrimidine metabolism
  E79.81	Aicardi-Goutieres syndrome
  E79.82	Hereditary xanthinuria
  E79.89	Other specified disorders of purine and pyrimidine metabolism
  E79.9	Disorder of purine and pyrimidine metabolism, unspecified

Created by Peter Blahut, MD